Enzyme or Coenzyme
Isovaleryl-CoA Dehydrogenase
AMW:CHEM:081122A mitochondrial flavoprotein, this enzyme catalyzes the oxidation of 3-methylbutanoyl-CoA to 3-methylbut-2-enoyl-CoA using FAD as a cofactor. Defects in the enzyme, is associated with isovaleric acidemia (IVA).
Biochemistry
biochemical